HEREDITORY GINGIVAL FIBROMATOSIS IN A 7-YEAR-OLD GIRL: A CASE REPORT
This paper presents a case of hereditary gingival fibromatosis, a rarely reported disorder and addresses the complex nature of oral diagnosis,
treatment and long-term case management in the hereditary form of recurrent gingival fibromatosis. Case management is discussed in relation to
a 7-year-old girl who presented with recurrent, progressive gingival enlargement requiring consecutive periodontal treatment. The initial course of
treatment included 4-quadrant gingivectomy with excisional bevel incisions, followed by microscopic examination of the gingivectomy specimens
which supported the clinical diagnosis. 1 year later, recurrence of the condition was observed in all quadrants. It is recommended that patients with
this condition be monitored closely after gingivectomy so that the treatment requirements of localized areas can be addressed as needed.
Keywords: Heredity, Genome, Phenotype, Chromosome, Autosomal inheritance.
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Fig. 1: Facial profile of the patient
Fig. 2: Intraoral view of maxilla and mandible showing the presence excessive gingival overgrowth
Fig. 3: The orthopantomograph revealed presence of normal permanent tooth buds, improper occlusion, and partially erupted 22, 12 16, and 26
Fig. 4: (a and b) The microscopic picture of hereditary gingival fibromatosis
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